Serveur d'exploration sur le lymphœdème

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Severe lymphatic microangiopathy in Fabry disease.

Identifieur interne : 008E00 ( Main/Exploration ); précédent : 008D99; suivant : 008E01

Severe lymphatic microangiopathy in Fabry disease.

Auteurs : Beatrice R. Amann-Vesti [Suisse] ; Gabriele Gitzelmann ; Urs Widmer ; Nils U. Bosshard ; Beat Steinmann ; Renate Koppensteiner

Source :

RBID : pubmed:15624436

Descripteurs français

English descriptors

Abstract

Lymphedema has been described in a few cases of Fabry disease. The etiology of lymphedema in Fabry disease is unknown. The aim of the study was to evaluate morphology and function of lymphatic microvessels in this disease.

DOI: 10.1089/153968503768330229
PubMed: 15624436


Affiliations:


Links toward previous steps (curation, corpus...)


Le document en format XML

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<title xml:lang="en">Severe lymphatic microangiopathy in Fabry disease.</title>
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<name sortKey="Amann Vesti, Beatrice R" sort="Amann Vesti, Beatrice R" uniqKey="Amann Vesti B" first="Beatrice R" last="Amann-Vesti">Beatrice R. Amann-Vesti</name>
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<nlm:affiliation>University Hospital of Zurich, Zurich, Switzerland. beatrice.amann@usz.ch</nlm:affiliation>
<country xml:lang="fr">Suisse</country>
<wicri:regionArea>University Hospital of Zurich, Zurich</wicri:regionArea>
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<name sortKey="Gitzelmann, Gabriele" sort="Gitzelmann, Gabriele" uniqKey="Gitzelmann G" first="Gabriele" last="Gitzelmann">Gabriele Gitzelmann</name>
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<name sortKey="Bosshard, Nils U" sort="Bosshard, Nils U" uniqKey="Bosshard N" first="Nils U" last="Bosshard">Nils U. Bosshard</name>
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<name sortKey="Steinmann, Beat" sort="Steinmann, Beat" uniqKey="Steinmann B" first="Beat" last="Steinmann">Beat Steinmann</name>
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<name sortKey="Bosshard, Nils U" sort="Bosshard, Nils U" uniqKey="Bosshard N" first="Nils U" last="Bosshard">Nils U. Bosshard</name>
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<name sortKey="Steinmann, Beat" sort="Steinmann, Beat" uniqKey="Steinmann B" first="Beat" last="Steinmann">Beat Steinmann</name>
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<name sortKey="Koppensteiner, Renate" sort="Koppensteiner, Renate" uniqKey="Koppensteiner R" first="Renate" last="Koppensteiner">Renate Koppensteiner</name>
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<title level="j">Lymphatic research and biology</title>
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<term>Adolescent</term>
<term>Adult</term>
<term>Capillaries (pathology)</term>
<term>Endothelium, Lymphatic (pathology)</term>
<term>Fabry Disease (diagnosis)</term>
<term>Fabry Disease (genetics)</term>
<term>Fabry Disease (pathology)</term>
<term>Female</term>
<term>Heterozygote</term>
<term>Humans</term>
<term>Lymph</term>
<term>Lymphatic Vessels (pathology)</term>
<term>Lymphedema (pathology)</term>
<term>Lymphography (methods)</term>
<term>Male</term>
<term>Microcirculation</term>
<term>Microscopy, Fluorescence</term>
<term>Middle Aged</term>
<term>Pressure</term>
<term>Sex Factors</term>
<term>Skin (pathology)</term>
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<term>Adolescent</term>
<term>Adulte</term>
<term>Adulte d'âge moyen</term>
<term>Endothélium lymphatique (anatomopathologie)</term>
<term>Facteurs sexuels</term>
<term>Femelle</term>
<term>Humains</term>
<term>Hétérozygote</term>
<term>Lymphe</term>
<term>Lymphoedème (anatomopathologie)</term>
<term>Lymphographie ()</term>
<term>Maladie de Fabry (anatomopathologie)</term>
<term>Maladie de Fabry (diagnostic)</term>
<term>Maladie de Fabry (génétique)</term>
<term>Microcirculation</term>
<term>Microscopie de fluorescence</term>
<term>Mâle</term>
<term>Peau (anatomopathologie)</term>
<term>Pression</term>
<term>Vaisseaux capillaires (anatomopathologie)</term>
<term>Vaisseaux lymphatiques (anatomopathologie)</term>
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<term>Endothélium lymphatique</term>
<term>Lymphoedème</term>
<term>Maladie de Fabry</term>
<term>Peau</term>
<term>Vaisseaux capillaires</term>
<term>Vaisseaux lymphatiques</term>
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<keywords scheme="MESH" qualifier="diagnosis" xml:lang="en">
<term>Fabry Disease</term>
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<keywords scheme="MESH" qualifier="diagnostic" xml:lang="fr">
<term>Maladie de Fabry</term>
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<term>Fabry Disease</term>
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<keywords scheme="MESH" qualifier="génétique" xml:lang="fr">
<term>Maladie de Fabry</term>
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<term>Lymphography</term>
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<keywords scheme="MESH" qualifier="pathology" xml:lang="en">
<term>Capillaries</term>
<term>Endothelium, Lymphatic</term>
<term>Fabry Disease</term>
<term>Lymphatic Vessels</term>
<term>Lymphedema</term>
<term>Skin</term>
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<keywords scheme="MESH" xml:lang="en">
<term>Adolescent</term>
<term>Adult</term>
<term>Female</term>
<term>Heterozygote</term>
<term>Humans</term>
<term>Lymph</term>
<term>Male</term>
<term>Microcirculation</term>
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<term>Facteurs sexuels</term>
<term>Femelle</term>
<term>Humains</term>
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<term>Lymphe</term>
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<front>
<div type="abstract" xml:lang="en">Lymphedema has been described in a few cases of Fabry disease. The etiology of lymphedema in Fabry disease is unknown. The aim of the study was to evaluate morphology and function of lymphatic microvessels in this disease.</div>
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<name sortKey="Bosshard, Nils U" sort="Bosshard, Nils U" uniqKey="Bosshard N" first="Nils U" last="Bosshard">Nils U. Bosshard</name>
<name sortKey="Gitzelmann, Gabriele" sort="Gitzelmann, Gabriele" uniqKey="Gitzelmann G" first="Gabriele" last="Gitzelmann">Gabriele Gitzelmann</name>
<name sortKey="Koppensteiner, Renate" sort="Koppensteiner, Renate" uniqKey="Koppensteiner R" first="Renate" last="Koppensteiner">Renate Koppensteiner</name>
<name sortKey="Steinmann, Beat" sort="Steinmann, Beat" uniqKey="Steinmann B" first="Beat" last="Steinmann">Beat Steinmann</name>
<name sortKey="Widmer, Urs" sort="Widmer, Urs" uniqKey="Widmer U" first="Urs" last="Widmer">Urs Widmer</name>
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